ОСОБЕННОСТИ ВЕДЕНИЯ ДЕТЕЙ С АНОМАЛИЕЙ ПИТЕРСА

Аннотация

Peters' anomaly is a rare congenita I disorder of the anterior segment of the eye characterized hy centra! cornea! opacities of variable size with associated defects in the posterior stroma, Descemel's membrane, and endothelium, /n Peters anomaly, iridocorneal adhesions are usually attached to the edge of the corneal opacities. The incidence of the disease in the population is 1:200,000. Approximately 700 people, in Russia, 1500 people, in the CIS and 35,000 people, all over the world have Peters anomaly. Target. To study the features of managing children with Peters anomaly based on materials from the clinic of the Tashkent Pediatric Medical Institute (TashPMl). .Material and methods. Under our supervision in the eye department of the TashPMl clinic there were 12 children (19 eyes) with Peters anomaly aged 2 months and older, up to 2 years. Result and discussion. The mesodermal form of Peters' anomaly (type I) was observed in 4 children (6 eyes), the ectodermal form (type 2) - in 8 children (13 eyes). In patients with type 1 Peters anomaly, an increase in IOP was observed in 33% of cases. In patients with type 2 Peters anomaly, in addition to opacification, changes in the lens were also observed. An increase in IOP was observed in 75% of cases. To treat concomitant glaucoma, patients with type I Peters anomaly underwent the following types of surgical interventions: sinustrabeculectomy, iridocycloretraction. Patients with type 2 Peters anomaly undergo reconstructive surgery, including reconstruction of the anterior chamber with surgical dissection of the anterior fusions, if necessary, in combination with aspiration of congenital cataracts. In 89% of cases, an organ-preserving, anatomical-reconstructive effect was achieved. Conclusion. Peters' anomaly is a serious congenital pathology' that requires timely implementation of a full range of diagnostic measures and early antiglaucomatous and optical-reconstructive operations.