CLINICAL AND NEUROLOGICAL CHARACTERISTICS OF CHILDREN WITH HEREDITARY SPASTIC PARAPLEGIA OF STRUMPEL IN COMPARATIVE ASPECT WITH CEREBRAL PALSY OF SPASTIC DIPLEGIA

Аннотация

We compared the clinical and neurological picture of hereditary spastic paraplegia (HSP) and cerebral palsy of spastic diplegia. The results of a neurological examination indicate that in patients in the comparison group, clinical symptoms, especially changes in the cranial innervation and motor sphere, were more pronounced compared to the main group. During a clinical and neurological examination of patients with HSP, we identified both pure spastic paraplegia, characterized only by motor disorders (71.5%), and spastic paraplegia with complications (20%) in the form of dysfunction of the cranial nerves, intellectual impairment of varying degrees (5.4%), pelvic organ dysfunction (4.4%), history of seizures (5.2%), polyneuropathies (3.15%), extraneural symptoms were detected in 3 (3.1%) patients, i.e. congenital skin changes in the form of ichthyosis.